RT Journal Article
SR Electronic
T1 Spontaneous bilateral chylothorax with fatal outcome in a patient with melorheostosis
JF Saudi Medical Journal
JO Saudi Med J
FD Prince Sultan Military Medical City
SP 1666
OP 1668
VO 29
IS 11
A1 Leuenberger, Michele
A1 Braunwalder, Jan
A1 Schmid, Ralph A.
A1 Stanga, Zeno
YR 2008
UL http://smj.org.sa/content/29/11/1666.abstract
AB We report a case of progressive, multifocal melorheostosis in a 28-year-old woman, with involvement of the left arm, chest, spine, and impressive soft tissue involvement. In the past, she had undergone multiple vascular interventions. She presented with spontaneous massive bilateral chylothorax. After conservative treatment without success, we conducted bilateral pleurodesis. This resulted in a clear reduction of pleural effusions, but her medical condition subsequently worsened due to progressive parenchymatous infiltrates, and increased interlobal pleural effusions. She ultimately died of global respiratory insufficiency. In patients with melorheostosis, involvement of the soft tissue can result in distinctive morbidity, and whenever possible, treatment should be conservative.