PT  - JOURNAL ARTICLE
AU  - Al-Jahdali, Hamdan H.
AU  - Al-Shirawi, Nehad N.
AU  - Bamefleh, Hana S.
AU  - Yamani, Nizar M.
TI  - Sinus histiocytosis with massive lymphadenopathy Rosai-Dorfman's Disease as cause of isolated hilar lymphadenopathy and complete remission after high dose steroid
DP  - 2008 May 01
TA  - Saudi Medical Journal
PG  - 763--765
VI  - 29
IP  - 5
4099  - http://smj.org.sa/content/29/5/763.short
4100  - http://smj.org.sa/content/29/5/763.full
SO  - Saudi Med J2008 May 01; 29
AB  - Rosai-Dorfman's Disease, also known as sinus histiocytosis with massive lymphadenopathy SHML, is a rare histiocytic proliferative disorder and a distinct clinico-pathological feature of unknown origin. Painless cervical lymphadenopathy is the most common clinical presentation. Different treatment modalities have been tried with variable responses, however, there is no consensus on the best modality of treatment. Here, we present a case report of SHML causing isolated hilar lymphadenopathy with complete remission for more than 6 years, after a short course of high dose steroid dexamethasone 20 mg daily for 3 days.