RT Journal Article
SR Electronic
T1 Sinus histiocytosis with massive lymphadenopathy Rosai-Dorfman's Disease as cause of isolated hilar lymphadenopathy and complete remission after high dose steroid
JF Saudi Medical Journal
JO Saudi Med J
FD Prince Sultan Military Medical City
SP 763
OP 765
VO 29
IS 5
A1 Al-Jahdali, Hamdan H.
A1 Al-Shirawi, Nehad N.
A1 Bamefleh, Hana S.
A1 Yamani, Nizar M.
YR 2008
UL http://smj.org.sa/content/29/5/763.abstract
AB Rosai-Dorfman's Disease, also known as sinus histiocytosis with massive lymphadenopathy SHML, is a rare histiocytic proliferative disorder and a distinct clinico-pathological feature of unknown origin. Painless cervical lymphadenopathy is the most common clinical presentation. Different treatment modalities have been tried with variable responses, however, there is no consensus on the best modality of treatment. Here, we present a case report of SHML causing isolated hilar lymphadenopathy with complete remission for more than 6 years, after a short course of high dose steroid dexamethasone 20 mg daily for 3 days.