PT - JOURNAL ARTICLE AU - Almusally, Rayyan M. TI - Right lung hypoplasia associated with polysplenia AID - 10.15537/smj.2024.45.9.20240265 DP - 2024 Sep 01 TA - Saudi Medical Journal PG - 959--962 VI - 45 IP - 9 4099 - http://smj.org.sa/content/45/9/959.short 4100 - http://smj.org.sa/content/45/9/959.full SO - Saudi Med J2024 Sep 01; 45 AB - Pulmonary agenesis is a very rare congenital abnormality that can be missed in a routine radiographic examination, which delays diagnosis until adulthood. It can be associated with other congenital malformations, such as valvular heart disease and gastrointestinal organ abnormalities. Computed tomography (CT) is a useful modality for its better delineation of pulmonary and vascular structures. The reported case here is for an adult male who presented with dextroposition of the heart and was found to have a unilobed right lung associated with polysplenia. This has not been previously reported in the literature.