PT  - JOURNAL ARTICLE
AU  - Baztarrica, Gabriel E.
AU  - Sereno, Gastón G.
AU  - Villecco, Sebastían A.
AU  - Porcile, Rafael
TI  - Ventricular tachycardia an atypical presentation of Ebstein’s disease
DP  - 2014 Dec 01
TA  - Saudi Medical Journal
PG  - 1510--1512
VI  - 35
IP  - 12
4099  - http://smj.org.sa/content/35/12/1510.short
4100  - http://smj.org.sa/content/35/12/1510.full
SO  - Saudi Med J2014 Dec 01; 35
AB  - Ebstein’s anomaly (EA) is a rare congenital malformation, characterized by an apical displacement and dysplasia of the septal leaflet of the tricuspid valve with a right ventricular atrialization compromising its function. This malformation includes electrical conduction abnormalities, and very rarely ventricular arrhythmias. We report the case of a 22-year-old male, presenting with dizziness and palpitations. The electrocardiogram showed a sustained monomorphic ventricular tachycardia (SMVT). The presentation of the disease with ventricular tachycardia associated with hemodynamic instability is extremely rare. We placed a surgical implantable cardiac defibrillator when the diagnosis of EA, SMVT, and right ventricular systolic impairment was confirmed.