RT Journal Article
SR Electronic
T1 Ventricular tachycardia an atypical presentation of Ebstein’s disease
JF Saudi Medical Journal
JO Saudi Med J
FD Prince Sultan Military Medical City
SP 1510
OP 1512
VO 35
IS 12
A1 Baztarrica, Gabriel E.
A1 Sereno, Gastón G.
A1 Villecco, Sebastían A.
A1 Porcile, Rafael
YR 2014
UL http://smj.org.sa/content/35/12/1510.abstract
AB Ebstein’s anomaly (EA) is a rare congenital malformation, characterized by an apical displacement and dysplasia of the septal leaflet of the tricuspid valve with a right ventricular atrialization compromising its function. This malformation includes electrical conduction abnormalities, and very rarely ventricular arrhythmias. We report the case of a 22-year-old male, presenting with dizziness and palpitations. The electrocardiogram showed a sustained monomorphic ventricular tachycardia (SMVT). The presentation of the disease with ventricular tachycardia associated with hemodynamic instability is extremely rare. We placed a surgical implantable cardiac defibrillator when the diagnosis of EA, SMVT, and right ventricular systolic impairment was confirmed.