RT Journal Article
SR Electronic
T1 Pulmonary lymphangioleiomyomatosis
JF Saudi Medical Journal
JO Saudi Med J
FD Prince Sultan Military Medical City
SP 131
OP 134
VO 28
IS 1
A1 Hilal B. Shawki
A1 Shakir M. Muhammed
A1 Amal N. Reda
A1 Thair S. Abdulla
A1 Delaram M. Ardalan
YR 2007
UL http://smj.org.sa/content/28/1/131.abstract
AB A 38-year-old Iraqi female, presented with one-year history of exertional dyspnea and exercise intolerance, without systemic or constitutional symptoms. Clinical examination revealed bilateral basal crackles with signs suggestive of left side pleural effusion, chest x-ray showed left sided pleural effusion, and diffuse bilateral basal pulmonary shadowing. Her biochemical analysis, hematological tests, electrocardiogram and echocardiography were normal, aspiration of the fluid revealed a chylothorax, the radiological shadowing was proved by computed tomography scan of the chest to be diffuse cystic lesions involving mostly the lower lobes. Open lung biopsy showed dilated lymphatic vessels with surrounding inflammatory cells and smooth muscle fibers consistently with the diagnosis of pulmonary lymphangioleiomyomatosis LAM.