Table 4

- Types of bacterial colonization from the first respiratory culture in patients with CF with common CFTR variants.

Variant numbercDNA NameFirst respiratory culture
1c.1521_1523delCTTStreptococcus pneumoniae
Pseudomonas aeruginosa
Haemophilus influenzae
Escherichia coli
Klebsiella sp.
Branhamella catarrhalis
Aspergillus sp.
Pseudomonas sp.
2c.1418delGPseudomonas aeruginosa
Haemophilus influenzae
Streptococcus pneumoniae
Staphylococcus aureus
3c.579+G>TStreptococcus pneumoniae
Haemophilus influenzae
Pseudomonas aeruginosa
Branhamella catarrhalis
Pseudomonas aeruginosa
Klebsiella pneumoniae
4c.2988+1G>APseudomonas aeruginosa
Streptococcus pneumoniae
Pseudomonas aeruginosa
Branhamella catarrhalis
Staphylococcus aureus
5c.3419T>AStaphylococcus aureus
6c.4124A>CStenotrophomonas maltophilia
Enterobacter cloacae
  • CFTR: cystic fibrosis transmembrane conductance regulator, cDNA: complementary deoxyribonucleic acid