Table 1

- Distribution of studied patients according to their demographics, comorbidity and family history of hearing loss (N=33).

Variablen (%)
Age (mean 9 years, 108 months)
Pediatric (mean 3 years, 36 months)108 (81.2)
Adult (mean 36 years, 432 months)25 (18.8)
Gender
Female58 (43.6)
Male75 (56.4)
Nationality
Non-Saudi5 (3.8)
Saudi128 (96.2)
Residency
From Makkah67 (50.4)
From outside Makkah66 (49.6)
Comorbidity
No77 (74.0)
Yes27 (26.0)
If having comorbidity, specify ?(n=27)
Sudden sensory neural hearing loss (SSNHL)5 (3.8)
Consanguinity10 (7.5)
Cochlear implantation24 (18)
Cardiac disease7 (5.3)
Dihydrolipoamide dehydrogenase (DLD)3 (2.3)
Enlarged vestibular aqueduct syndrome (EVAS)3 (2.3)
Epilepsy2 (1.5)
Pierre Roben sequel4 (3.0)
Cogan syndrome2 (1.6)
Other26 (19.5)
Family history of hearing loss
No107 (80.5)
Yes26 (19.5)