Reversible hypertrophic cardiomyopathy associated with nesidioblastosis

J Pediatr. 1992 Feb;120(2 Pt 1):272-5. doi: 10.1016/s0022-3476(05)80442-1.

Abstract

An infant with persistent hyperinsulinism had hypertrophic cardiomyopathy that progressed until near-total pancreatectomy was performed. After pancreatectomy the condition resolved. Hyperinsulinism may be a cause of treatable cardiomyopathy.

Publication types

  • Case Reports

MeSH terms

  • Cardiomyopathy, Hypertrophic / congenital
  • Cardiomyopathy, Hypertrophic / diagnosis
  • Cardiomyopathy, Hypertrophic / etiology*
  • Heart Failure / etiology
  • Humans
  • Infant
  • Insulin / blood
  • Male
  • Pancreatectomy
  • Pancreatic Diseases / blood
  • Pancreatic Diseases / complications*
  • Pancreatic Diseases / congenital
  • Pancreatic Diseases / surgery

Substances

  • Insulin