Fasting hypoglycaemia and metabolic acidosis associated with deficiency of hepatic fructose-1,6-diphosphatase activity

Lancet. 1970 Jul 4;2(7662):13-6. doi: 10.1016/s0140-6736(70)92474-8.
No abstract available

MeSH terms

  • Acidosis / etiology*
  • Aldehyde-Lyases / metabolism
  • Blood Glucose / analysis
  • Carbohydrate Metabolism, Inborn Errors / enzymology*
  • Child, Preschool
  • Fasting*
  • Female
  • Fructose / metabolism
  • Galactose / metabolism
  • Gluconeogenesis
  • Glucose Tolerance Test
  • Glycerol / pharmacology
  • Glycolysis
  • Humans
  • Hypoglycemia / etiology*
  • Liver Glycogen / metabolism
  • Liver* / pathology
  • Phosphoric Monoester Hydrolases / metabolism*

Substances

  • Blood Glucose
  • Liver Glycogen
  • Fructose
  • Phosphoric Monoester Hydrolases
  • Aldehyde-Lyases
  • Glycerol
  • Galactose